Creutzfeldt-Jakob disease (CJD) is a transmissible, rapidly progressing, fatal neurodegenerative disorder called a spongioform degeneration that seems to be related to “mad cow disease.”

Creutzfeldt-Jakob disease (CJD) affects many areas of the brain. At UCSF, CJD is sometimes called the “great mimicker” because it causes symptoms that occur in many other neurological diseases. …    



Creutzfeldt-Jakob Disease

Creutzfeldt-Jakob disease is an unusual neurologic disorder, with a prevalence of approximately 1 case per million population, which is about 1/10,000 that of Alzheimer’s disease. Creutzfeldt-Jakob disease has captured widespread attention, in part because of the recent epidemic of bovine spongiform encephalopathy (“mad cow disease”) and the appearance of 139 cases of “new-variant” Creutzfeldt-Jakob…